Keratosis follicularis spinulosa decalvans is a rare X-linked disorder described by Siemens in 1926.
It is a disease that begins in infancy with keratosis pilaris localized on the face, then evolves to more diffuse involvement.
[1]: 580, 762 [2]: 649, 714 [3] An association with SAT1 has been suggested.
[4] see also Template:Congenital malformations and deformations of skin appendages, Template:Phakomatoses, Template:Pigmentation disorders, Template:DNA replication and repair-deficiency disorder
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