Common presenting symptoms include abdominal pain, emesis, and jaundice.
A multidisciplinary approach including good clinical history, state of the art imaging, and careful pathology is often needed to establish the correct diagnosis.
[5] If the tumor is operable, the first line of therapy should be surgical resection.
Then, after surgical resection, adjuvant chemotherapy should be given, even in stage I disease.
[6] A multi-disciplinary approach to the treatment, including surgeons, oncologists, pathologists, radiologists, and radiation oncologists, is often the best approach to managing these patients.