The pathological findings consist of an abundance of ganglion cells in both dilated and narrow areas of the intestine.

All had marked dilatation of the bladder and some had hydronephrosis and the external appearance of prune belly.

[5] Berdon syndrome is generally diagnosed after birth by the signs and symptoms as well as radiological and surgical findings.

[6] Long-term survival with Berdon syndrome usually requires parenteral nutrition and urinary catheterisation or diversion.

[7] A multivisceral transplant (stomach, pancreas, small bowel, liver and large intestine) has also been successful.