Pityriasis rubra pilaris refers to a group of chronic disorders characterized by reddish orange, scaling plaques and keratotic follicular papules.

For some, early symptoms may also include generalized swelling of the legs, feet and other parts of the body.

The inherited form starts early in childhood with persistent long-term symptoms into adulthood.

Application of lubricants under plastic occlusion before bedtime appears to aid removal of scales on hands and feet.

The most effective therapy is long term use of oral retinoids, such as acitretin and isotretinoin.