Their origin is currently unknown, but they may be produced by budding from the external root sheath as a genetically determined structural aberration.
They arise preferentially in areas of high hair follicle concentrations, so 90% of cases occur on the scalp.
[10] Histologically, they are lined by stratified squamous epithelium that lacks a granular cell layer and are filled with compact "wet" keratin.
The tumor is clinically benign, although it may display nuclear atypia, dyskeratotic cells, and mitotic figures.
This method is best performed on cysts larger than a pea that have formed a thick enough wall to be easily identified after the sac is emptied.