[2] Ewing’s sarcoma is most common in Caucasians and typically diagnosed during the first several decades of life, most often in someone’s teens.
The most common presenting symptom is pain in the bone, and the initial diagnostic step is imaging, often both MRI and radiograph.
The current practice for treatment is first neoadjuvant radiation to shrink the cancer, resection, and follow up chemotherapy.
Treatment also consists of surgical removal followed by chemotherapy, however patients seem to do better overall when compared to Ewing’s sarcoma of the bone.
[8][9] Treatment of PNETs is the same as extra-osseous Ewing’s sarcoma, with resection of the whole tumor alongside chemotherapy and radiation.
Outcomes however are poor as PNET remains an aggressive cancer as a member of the Ewing Family of Tumors.