Carnitine palmitoyltransferase II

137612896ENSG00000157184ENSMUSG00000028607P23786P52825NM_000098NM_001330589NM_009949NP_000089NP_001317518NP_034079Carnitine O-palmitoyltransferase 2, mitochondrial is an enzyme that in humans is encoded by the CPT2 gene.

[5][6] Carnitine palmitoyltransferase II precursor (CPT2) is a mitochondrial membrane protein which is transported to the mitochondrial inner membrane.

CPT2 together with carnitine palmitoyltransferase I oxidizes long-chain fatty acids in the mitochondria.

Defects in this gene are associated with mitochondrial long-chain fatty-acid (LCFA) oxidation disorders and carnitine palmitoyltransferase II deficiency.

[6]

Acyl-CoA from cytosol to the mitochondrial matrix