Patients show visible folds, ridges or creases on the surface of the top of the scalp.

Dermatological examination reveals the presence of thickened skin folds and furrows that are most commonly found on the vertex and occipital regions of the scalp.

In some cases, additional tests may be conducted to rule out underlying conditions, especially for secondary CVG, including hormonal assays, imaging studies, or biopsy to assess the scalp's histological features.

[11] Primary non-essential CVG can be associated with neuropsychiatric disorders including cerebral palsy, epilepsy, seizures, and ophthalmologic abnormalities, most commonly cataracts.

[citation needed] Secondary CVG occurs as a consequence of a number of diseases or drugs that produce changes in scalp structure.

It may also arise in association with melanocytic naevi (moles), birthmarks (including connective tissue naevi, fibromas and naevus lipomatosus), and inflammatory processes (e.g. eczema, psoriasis, Darier disease, folliculitis, impetigo, atopic dermatitis, acne).

[citation needed] Options for medical treatment for this condition have been limited to plastic surgery with excision of the folds by means of scalp reduction/surgical resection.