Diktyoma

[1][2] Other signs and symptoms include lens subluxation, glaucoma, cataract, exophthalmos, buphthalmos, strabismus, and ptosis.

[3] Based on histology, the tumor is classified as malignant if it contains poorly differentiated neuroblasts, nuclear pleomorphism, markedly abnormal mitotic activity, sarcomatous components, or invasion into the uvea, cornea, or sclera.

[5][6] Ultrasound is excellent for demonstrating cystic collections of vitreous fluid in the tumor, and may show calcifications in the teratoid type.

On CT, diktyomas typically appear as dense, irregular masses in the ciliary body, which enhances with administration of intravenous contrast material.

[4][6] On MRI, diktyomas typically appear slightly to moderately hyperdense to vitreous on T1-weighted images and hypodense on T2-weighted images, with marked homogeneous enhancement (except for prominent parts of cystic components, which, if present, may impart heterogeneity) after administration of intravenous contrast material.

[8] Grossly, the tumor appears white, gray, or yellow, with irregular surface, often studded with small cysts.

[4][6] Tumor cells form a characteristic diktyomatous pattern, with folded cords and sheets resembling a fisherman's net.

Proliferating tumor cells of diktyoma maintain the same polarity, arranged in cords and sheets folding back upon themselves.