Papuloerythroderma of Ofuji

Papuloerythroderma of Ofuji is a rare disorder most commonly found in Japan, characterized by pruritic papules that spare the skinfolds, producing bands of uninvolved cutis, creating the so-called deck-chair sign.

Frequently there is associated blood eosinophilia.

Skin biopsies reveal a dense lymphohistiocytic infiltrate, eosinophils in the papillary dermis, and increased Langerhans cells (S-100 positive).

Systemic steroids are the treatment of choice and may result in long-term remissions.

[5] This cutaneous condition article is a stub.