Both women and Caucasian individuals show a minor prevalence regarding neuroendocrine tumor diagnosis without an explanation.

[15] Small neuroendocrine tumors[16] (<2 cm) without features of malignancy may be treated by appendectomy if complete removal is possible.

The peritoneal cavity is infused with heated chemotherapy known as HIPEC in an attempt to eradicate residual disease.

[17] A study of primary malignancies in the United States found a rate of 0.12 cases per 1,000,000 population per year.

One theory proposed is the increased use of computed tomography imaging in emergency departments since the early 1990s allowing for detection to occur before a surgery may be performed.