[2] The disease creates lesions in the brain and increases cerebrospinal fluid volume, resulting in hydrocephalus.

They sometimes occur in conjunction with other hereditary cancers, including Li–Fraumeni syndrome and malignant rhabdoid tumors.

[6] Choroid plexus carcinomas can induce hydrocephalus through a variety of mechanisms, including blockage of normal cerebrospinal fluid (CSF) flow, the tumor overproducing CSF, spontaneous hemorrhage, and expansion of the ventricles.

[8] Treatment of choroid plexus carcinoma depends on the location and severity of the tumor.

The best outcomes occur when total resection of the tumor is combined with adjuvant chemotherapy and radiotherapy.