Glycogen storage disease type IX is a hereditary deficiency of glycogen phosphorylase kinase B that affects the liver and skeletal muscle tissue.

[1] The signs and symptoms in glycogen storage disease type IX include:[1] Most of these signs and symptoms diminish as adulthood sets in.

[medical citation needed] The management of Glycogen storage disease IX requires treatment of symptoms by frequent intake of complex carbohydrates and protein to combat the low blood sugar.

Liver function is regularly monitored and problems managed as they arise.

Routine checks of metabolism are needed to ensure blood sugar (glucose) and ketones are managed.