HGSNAT

13805052120ENSG00000165102ENSMUSG00000037260Q68CP4Q3UDW8NM_152419NM_001363227NM_001363228NM_001363229NM_025070NM_029884NM_133970NP_689632NP_001350156NP_001350157NP_001350158NP_084160Heparan-α-glucosaminide N-acetyltransferase (also called "acetyl-CoA:heparan-α-D-glucosaminide N-acetyltransferase" and "acetyl-CoA:alpha-glucosaminide N-acetyltransferase") is an enzyme that in humans is encoded by the HGSNAT gene.

[5][6][7] In enzymology, this enzyme belongs to the family of transferases, specifically those acyltransferases transferring groups other than aminoacyl groups.

It is catalysed in the chemical reaction: This enzyme participates in glycosaminoglycan degradation and glycan structures degradation.

Mutations in the gene encoding this enzyme cause mucopolysaccharidosis IIIC.

[6]