[3] The primary defect lies in the inability of the lymphatic system to adequately drain lymph, resulting in its subsequent accumulation and leakage into the intestinal lumen.

[4] The overflow of lymphatic fluid into the intestines leads to the loss of lymphocytes, immunoglobulins, and proteins, causing lymphopenia, hypogammaglobulinemia, and hypoalbuminemia, respectively.

[4] Patients with intestinal lymphangiectasia present with a range of symptoms, significantly influenced by the extent of protein loss.

[4] Nutritional deficiencies may develop due to malabsorption, leading to growth retardation in children and weight loss in adults.

[4] Some patients may exhibit minimal or subtle clinical features, diverging from the "textbook" presentations often associated with severe cases in adults.

[10] Computerized tomography (CT) can show low attenuation material within the bowel walls which corresponds to lipid-containing chylous fluid within the dilated lymphatic vessels.

[11] In the case of primary intestinal lymphangiectasia, a diet of low-fat and high-protein aliments, supplemental calcium and certain vitamins has been shown to reduce symptom effects.