Syringomyelia is a generic term referring to a disorder in which a cyst or cavity forms within the spinal cord.
Signs of the disorder tend to develop slowly, although sudden onset may occur with coughing, straining, or myelopathy.
A syrinx may also cause disruptions in the parasympathetic and sympathetic nervous systems, leading to Horner syndrome, abnormal body temperature or sweating, bowel control issues, or other problems.
[7] Classically, syringomyelia spares the dorsal column/medial lemniscus of the spinal cord, leaving pressure, vibration, touch and proprioception intact in the upper extremities.
Here, symptoms usually begin between the ages of 25 and 40 and may worsen with straining, called a valsalva maneuver, or any activity that causes cerebrospinal fluid pressure to fluctuate suddenly.
Symptoms may appear months or even years after the initial injury, starting with pain, weakness, and sensory impairment originating at the site of trauma.
[13] The primary symptom of post-traumatic syringomyelia (often referred to using the abbreviation of PTS)[14] is pain, which may spread upward from the site of injury.
[citation needed] What can make PTS difficult to diagnose is the fact that symptoms can often first appear long after the actual cause of the syrinx occurred (e.g., a car accident occurring and then the patient first experiencing PTS symptoms such as pain, loss of sensation, and reduced ability on the skin to feel varying degrees of hot and cold a number of months after the car accident).
When fluid dissects into the surrounding white matter forming a cystic cavity or syrinx, the term syringomyelia is applied.
The MRI radiographer takes images of body anatomy, such as the brain and spinal cord, in vivid detail.
In addition, computed axial tomography (CT) scans of a patient's head may reveal the presence of tumors and other abnormalities such as hydrocephalus.
[20] Like MRI and CT scans, another test, called a myelogram, uses radiographs and requires a contrast medium to be injected into the subarachnoid space.
Symptoms are due to spinal cord damage and include pain, decreased sensation of touch, weakness, and loss of muscle tissue.
[22] Furthermore, evidence also suggests that impact injuries to the thorax area highly correlate with the occurrence of a cervical-located syrinx.
Surgery involving the spinal cord carries certain risks, and as with any medical treatment, the potential benefits have to be weighed against the possible complications.
Evaluation of the condition is necessary because syringomyelia can remain stationary for long periods of time, and in some cases progress rapidly.
[citation needed] In cases involving an Arnold–Chiari malformation, the main goal of surgery is to provide more space for the cerebellum at the base of the skull and upper cervical spine, without entering the brain or spinal cord.
This is done with a shunt, which uses tubes and valves to let cerebrospinal fluid (CSF) drain from the syrinx into another cavity within the body (usually the abdomen).
By continually draining the syrinx, a shunt can arrest the progression of symptoms and relieve pain, headache, and tightness.
There are risks of injury to the spinal cord, infection, drainage becoming blocked, and bleeding, and they do not always achieve the intended results.
Successful procedures expand the area around the cerebellum and spinal cord, improving the flow of cerebrospinal fluid and thereby reducing the syrinx.
Learning when these defects occur during the development of the fetus can help with the understanding of this and similar disorders, and may lead to preventive treatment that can stop the formation of some birth abnormalities.
CT scans allow physicians to see abnormalities in the brain, and other diagnostic tests have also improved greatly with the availability of new, non-toxic, contrast dyes.